Cystic Fibrosis

People with cystic fibrosis have special nutritional needs. They need higher amounts of most nutrients to stay healthy. It is important for people with cystic fibrosis to see an Accredited Practising Dietitian who can help to make sure nutritional needs are being met.

Cystic fibrosis is an inherited disease that results in problems with lung function and difficulty digesting food. It is extremely important that the special nutritional needs of those with cystic fibrosis be met in order for them to stay healthy. In people with cystic fibrosis, higher amounts of most nutrients are needed to maintain weight and stay healthy. However, poor appetite, fatigue and nausea often make it difficult to eat. This means that food and drinks must be chosen carefully to meet these special needs and stay well nourished. It is especially important that children with cystic fibrosis meet their nutritional needs in order to grow and develop normally.

Special dietary needs in cystic fibrosis

Some of the nutrients people with cystic fibrosis need more of are:

• energy (kilojoules)
• protein
• fat soluble vitamins
• salt and other electrolytes

The following ideas will help people with cystic fibrosis to meet their needs:

• eat a wide variety of foods from each food group
• eating small frequent meals and snacks to fit in more food throughout the day
• having full-cream milk drinks between meals
• adding more oil and margarine to food in cooking
• adding skim milk powder to soups, stews and drinks
• snacking on cheese or adding grated cheese to cooked foods

Often in cystic fibrosis, it is necessary for supplements and enzymes to be taken to help meet nutritional needs. Enzymes must be taken with meals to help food be digested. It is important that anyone with cystic fibrosis see an Accredited Practising Dietitian to ensure their special needs are being met. Dietary needs may change and nutritional advice may need to be modified accordingly.